Chordoma is a rare, slow growing malignant tumor that develops in the spine and skull bones. It is thought to form from the remnants of the notochord (a preliminary structure present in a developing baby in the womb, which eventually forms the spinal cord). The exact cause of a chordoma has not been established with certainty.
Chordomas are more common in adults than children. They can be life-threatening and difficult to treat and therefore require specialized follow-up care.
The most evident signs of a chordoma are pain and neurological changes. Symptoms typical to a skull-based chordoma include headache, issues with vision such as double vision, and pain in the neck region. Symptoms vary depending on the size of the tumor. For instance, a large chordoma may bring about changes in voice and speech, as well as changes in facial sensation or movement and swallowing function. Some other symptoms include weakness in the limbs, pain, body pain, and changes in the functioning of the bowel or the bladder.
Diagnosis involves imaging tests such as CT or MRI scans. Your doctor may recommend X-rays to determine the extent of bone damage due to the tumor.